Primary embryonal rhabdomyosarcoma of the kidney in an adult : A case report
نویسندگان
چکیده
Rhabdomyosarcoma (RMS) is a malignant skeletal muscle neoplasm. RMS can occur anywhere in the body and is the most common childhood sarcoma (1). Pediatric RMS is an aggressive neoplasm with deregulated cell cycle checkpoints, high genome instability, and oncongene ampli ication such as MYC family members (2). However, RMS rarely occurs in adults. Moreover, sarcomas of the kidney are rare soft tissue tumors comprising approximately 1% of all primary renal malignancies in adults (3). Primary renal RMS of adults is characterized by pleomorphic histology and poor prognosis, but is extremely unusual (4). Here, we report a case of adult primary renal RMS of the embryonal histopathologic subtype.
منابع مشابه
Primary embryonal rhabdomyosarcoma of the kidney in an adult：A case report
Primary rhabdomyosarcoma (RMS) of the kidney is a rare malignant mesenchymal tumor with an aggressive clinical course. Adult renal RMS is typically a pleomorphic histologic subtype and only a few cases have ever been reported. We herein present a new case of renal RMS of the embryonal histologic subtype in a 26-year-old woman.
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